Pulmonary atresia with intact ventricular septum and coronary cameral fistulae: an unusual finding of a subsystemic right ventricle.

TitlePulmonary atresia with intact ventricular septum and coronary cameral fistulae: an unusual finding of a subsystemic right ventricle.
Publication TypeJournal Article
Year of Publication2016
AuthorsMohan S, Weinberg PM, Glatz AC
JournalCardiol Young
Volume26
Issue5
Pagination979-82
Date Published2016 Jun
ISSN1467-1107
KeywordsCoronary Angiography, Coronary Sinus, Echocardiography, Fistula, Heart Defects, Congenital, Heart Ventricles, Humans, Infant, Newborn, Male, Pulmonary Atresia, Ventricular Septum
Abstract

We report the case of a neonate with pulmonary atresia with intact ventricular septum and coronary cameral fistulae despite having a subsystemic right ventricle. We review the literature on coronary cameral fistulae in this disease and right ventricle-dependent coronary circulation. We discuss the potential consequences of this physiology, including risk of adverse cardiovascular events that may impact risk stratification and surgical palliation.

DOI10.1017/S1047951115002711
Alternate JournalCardiol Young
PubMed ID26796991