Protein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog.

TitleProtein Losing Enteropathy After Fontan Operation: Glimpses of Clarity Through the Lifting Fog.
Publication TypeJournal Article
Year of Publication2020
AuthorsRychik J, Dodds KM, Goldberg D, Glatz AC, Fogel M, Rossano J, Chen J, Pinto E, Ravishankar C, Rand E, Rome JJ, Dori Y
JournalWorld J Pediatr Congenit Heart Surg
Volume11
Issue1
Pagination92-96
Date Published2020 Jan
ISSN2150-136X
Abstract

Fontan-associated protein losing enteropathy is a challenge to treat and is a major contributor to morbidity and mortality in patients with palliated single ventricle. Numerous strategies for management have been proposed, with confusion as to how best to stratify and implement care among the many treatments available. Medical management can be helpful in some, while novel lymphatic interventions hold potential for remission with good results. We review our institutional approach to protein losing enteropathy after Fontan operation and provide a suggested algorithm and pathway for effective care.

DOI10.1177/2150135119890555
Alternate JournalWorld J Pediatr Congenit Heart Surg
PubMed ID31835975